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OncoMatch/Clinical Trials/NCT06161519

PLX038 in Primary Central Nervous System Tumors Containing MYC or MYCN Amplifications

Is NCT06161519 recruiting? Yes, currently enrolling (May 2026). This Phase 1/2 trial studies PLX038 for glioma.

Phase 1/2RecruitingNational Cancer Institute (NCI)NCT06161519Data as of May 2026

Treatment: PLX038Background: About 90,000 new cases of brain and spinal cord tumors are diagnosed annually in the United States. Most of these tumors are benign; however, about 30% are malignant, and 35% of people with malignant tumors in the brain and spinal cord will die within 5 years. Many of these people have changes in certain genes (MYC or MYCN) that drive the development of their cancers. Objective: To test a study drug (PLX038) in people with tumors of the brain or spinal cord. Eligibility: People aged 18 years or older with a tumor of the brain or spinal cord. Some participants must also have tumors with changes in the MYC or MYCN genes. Design: Participants will be screened. They will have a physical exam and blood tests. They will have imaging scans and a test of their heart function. They may need to have a biopsy: A sample of tissue will be removed from their tumor. PLX038 is given through a tube attached to a needle inserted into a vein in the arm. All participants will receive PLX038 on the first day of each 21-day treatment cycle. They will take a second drug 3 days later to help reduce the risk of infection; for this drug, participants will be shown how to inject themselves under the skin at home. Blood tests, imaging scans, and other tests will be repeated during study visits. Hair samples will also be collected during these visits. Some participants may have an additional biopsy. Study treatment will continue up to 7 months. Follow-up visits will continue every few months for up to 5 years.

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Extracted eligibility criteria

Cancer type

Glioblastoma

Biomarker criteria

Required: MYCN amplification (fold change (FC) of >= 2.5X (5 copies) with a minimum tumor content of 20%)

MYCN amplified ependymoma

Required: MYCN amplification (fold change (FC) of >= 2.5X (5 copies) with a minimum tumor content of 20%)

MYCN amplified ependymoma (recurrent or progressive)

Required: MYCN amplification (fold change (FC) of >= 2.5X (5 copies) with a minimum tumor content of 20%)

medulloblastoma with MYCN amplification

Required: MYC amplification (fold change (FC) of >= 2.5X (5 copies) with a minimum tumor content of 20%)

medulloblastoma with MYC amplification

Required: MYCN amplification (fold change (FC) of >= 2.5X (5 copies) with a minimum tumor content of 20%)

any other recurrent or progressive primary CNS tumor with MYCN amplification

Required: MYC amplification (fold change (FC) of >= 2.5X (5 copies) with a minimum tumor content of 20%)

any other recurrent or progressive primary CNS tumor with MYC amplification

Required: MYCN wild-type

Any recurrent glioblastoma without MYC or MYCN amplifications

Required: MYC wild-type

Any recurrent glioblastoma without MYC or MYCN amplifications

Excluded: UGT1A1 *28 homozygous

Participants with history of homozygous for the UGT1A1*28 variant allele with severely reduced UGT1A1 activity

Prior therapy

Must have received: surgery and radiation therapy — newly diagnosed MYCN amplified ependymoma (Cohort Phase IIA)

must have completed surgery followed by radiation at least 4 weeks and no more than 10 weeks from the last dose of radiation prior to study treatment initiation

Must have received: cytotoxic chemotherapy or radiation therapy — Cohorts Phase I, Phase IIB, Phase IIC, and Phase IID

must have completed prior cytotoxic chemotherapy or radiation at least 4 weeks prior to study treatment initiation (at least 6 weeks if the last regimen included lomustine (CCNU) or carmustine (BCNU); at least 3 weeks if the last regimen included bevacizumab; at least 4 weeks if the last regimen included a checkpoint inhibitor or any other type of immunotherapy or cellular therapy; at least 5 half-lives if the last regimen included any investigational agent(s). Participants previously treated with PHOTON radiation to at least 2 segments of the spine must have completed radiation at least 12 months before study treatment initiation.

Cannot have received: pegylated topoisomerase inhibitor

History of treatment with pegylated topoisomerase inhibitors

Lab requirements

Blood counts

leukocytes >=3,000/microliter; absolute neutrophil count >1,500/microliter; platelets >100,000/microliter; hemoglobin >= 9 g/dL (may be transfused within 2 weeks prior to treatment to achieve this level)

Kidney function

creatinine within normal institutional limits OR eGFR >= 60 mL/min/1.73 m^2 for participants with creatinine levels above institutional normal

Liver function

total bilirubin within normal institutional limits; AST/ALT <2.5 X institutional upper limit of normal (ULN)

Participants must have adequate organ and marrow function as defined below: * leukocytes >=3,000/microliter * absolute neutrophil count >1,500/microliter * platelets >100,000/microliter * hemoglobin >= 9 g/ dL (may be transfused within 2 weeks prior to treatment to achieve this level) * total bilirubin within normal institutional limits * aspartate aminotransferase (AST) / alanine aminotransferase (ALT) <2.5 X institutional upper limit of normal (ULN) * creatinine within normal institutional limits OR * estimated glomerular filtrate rate (eGFR) using chronic kidney disease epidemiology collaboration) (CKD-EPI) equation:>= 60 mL/min/1.73 m^2 for participants with creatinine levels above institutional normal

Structured fields extracted by AI. May contain errors — verify against the official protocol.

US trial sites

  • National Institutes of Health Clinical Center · Bethesda, Maryland

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