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OncoMatch/Clinical Trials/NCT05843253

Study of Ribociclib and Everolimus in HGG and DIPG or Ribociclib and Temozolomide in DHG, H3G34-mutant

Is NCT05843253 recruiting? Yes, currently enrolling (Jun 2026). This Phase 2 trial studies multiple treatments including Ribociclib and Everolimus for high grade glioma.

Phase 2RecruitingNationwide Children's HospitalNCT05843253Data as of Jun 2026Location: International · 7 countries

Treatment: Ribociclib · Everolimus · Temozolomide (TMZ)The goal of this study is to determine the efficacy of the 1) ribociclib and everolimus to treat pediatric and young adult patients newly diagnosed with a high-grade glioma (HGG), including DIPG, that have genetic changes in pathways (cell cycle, PI3K/mTOR) that these drugs target or 2) ribociclib and temozolomide to treat pediatric and young adult patients newly diagnosed with diffuse hemispheric glioma (DHG), H3G34-mutant. The main question the study aims to answer is whether the combinations of ribociclib and everolimus or ribociclib and temozolomide can prolong the life of patients diagnosed with HGG/DIPG or DHG H3G34-mutant.

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Extracted eligibility criteria

Treatments studied

Targeted therapy

RibociclibEverolimus

Other

Temozolomide (TMZ)

Cancer type

Glioblastoma

Diffuse Intrinsic Pontine Glioma

Biomarker criteria

Required: CDK4 amplification

Amplification of CDK4

Required: CDK6 amplification

Amplification of CDK6

Required: CDKN2A deletion

Deletion of CDKN2A

Required: CDKN2B deletion

Deletion of CDKN2B

Required: CDKN2C deletion

Deletion of CDKN2C

Required: CCND1 amplification

Amplification of CCND1

Required: CCND2 amplification

Amplification of CCND2

Required: PTEN deletion

Deletion of PTEN

Required: PTEN mutation

Mutation of PTEN

Required: PIK3CA mutation

Mutation of PIK3CA

Required: PIK3CA amplification

Amplification of PIK3CA

Required: PIK3R1 mutation

Mutation of PIK3R1

Required: TSC1 deletion

Deletion of TSC1

Required: TSC1 mutation

Mutation of TSC1

Required: TSC2 deletion

Deletion of TSC2

Required: TSC2 mutation

Mutation of TSC2

Required: H3F3A (H3 K27M) H3G34R

For Stratum E: H3G34 (R/V) mutation

Required: H3F3A (H3 K27M) H3G34V

For Stratum E: H3G34 (R/V) mutation

Excluded: RB1 loss

Patients with evidence of homozygous (biallelic) RB1 loss by sequencing are excluded from TarGeT-A

Disease stage

Required: Stage WHO GRADE 3, WHO GRADE 4 (WHO)

All other HGGs must be WHO grade 3 or 4.

Demographics

Ages 1–39

Prior therapy

Must have received: radiation therapy (photon RT, proton RT) — HGG

Patients must have received photon or proton RT.

Cannot have received: anticancer therapy (other than surgery, RT, dexamethasone, temozolomide with RT, bevacizumab >21 days prior)

No other prior anticancer therapy for HGG will be allowed.

Lab requirements

Blood counts

ANC ≥ 1000/mm3; Platelet count ≥ 100,000/mm3 (transfusion independent); Hemoglobin >8 g/dL (may be transfused)

Kidney function

Creatinine clearance or radioisotope GFR ≥ 70ml/min/1.73 m2 OR age/gender-based maximum serum creatinine

Liver function

Total bilirubin ≤ 1.5x ULN for age; AST(SGOT)/ALT(SGPT) ≤ 3x ULN; serum albumin ≥ 2g/dL

Cardiac function

Ejection fraction ≥ 50% by echocardiogram; QTc ≤ 450 msec (Bazett formula)

Adequate Bone Marrow Function... Adequate Renal Function... Adequate Liver Function... Adequate Cardiac Function...

Structured fields extracted by AI. May contain errors — verify against the official protocol.

US trial sites

  • Children's Hospital Colorado · Aurora, Colorado
  • Children's National Medical Center · Washington D.C., District of Columbia
  • Ann & Robert H. Lurie Children's Hospital of Chicago · Chicago, Illinois
  • Dana-Farber Cancer Institute · Boston, Massachusetts
  • C.S. Mott Children's Hospital · Ann Arbor, Michigan

Showing up to 5 US sites.

See all sites on ClinicalTrials.gov →

Frequently asked questions

Is NCT05843253 currently recruiting?

Yes, this trial is currently recruiting patients.

Are there prior therapy exclusions?

Yes. Prior anticancer therapy (other than surgery, RT, dexamethasone, temozolomide with RT, bevacizumab >21 days prior) disqualifies patients from enrollment.

Does this trial require CDK4?

Yes, CDK4 amplification is a required biomarker for enrollment.

Does this trial require CDK6?

Yes, CDK6 amplification is a required biomarker for enrollment.

Does this trial require CDKN2A?

Yes, CDKN2A deletion is a required biomarker for enrollment.

Are patients with RB1 alterations eligible?

No. RB1 loss is an exclusion criterion.

What disease stage is eligible?

Stage WHO GRADE 3 or WHO GRADE 4 is required.

Is there an age limit?

Yes. Patients must be 39 years or younger and at least 1 years old.

Could you qualify for this trial?

Enter your biomarker results to see how this trial's eligibility criteria match your specific cancer profile.

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